Restrictive Pulmonary Disease (PEARLS)
The NCCPA™ PANCE Pulmonary Content Blueprint covers three types of restrictive pulmonary diseases
| Idiopathic pulmonary fibrosis |
Chronic progressive lung disorder characterized by increasing scarring, which ultimately reduces the capacity of the lungs; etiology unknown
- Physical exam: Inspiratory crackles
- CT: Diffuse, patchy fibrosis with pleural honeycombing, reticular opacities
FEV1/FVC ratio: Increased |
| Pneumoconiosis |
Any fibrosis of the lung tissues caused by dust in the lungs after prolonged environmental or occupational contact
- Asbestosis: shipbuilding and chest x-ray findings of interstitial fibrosis and pleural thickening
- Silicosis: mines and "eggshell" calcification of hilar lymph nodes
- Berylliosis: aerospace, electrical plants
- Coal Worker's Pneumoconiosis: coal miners, CXR demonstrates nodular opacities
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| Sarcoidosis |
Chronic autoimmune inflammatory disease in which small nodules (granulomas) develop in lungs, lymph nodes, and other organs
↑ ACE levels + Bilateral hilar adenopathy
Presentation:
- Pulmonary manifestations (most common), erythema nodosum, parotid gland enlargement
- Chest radiograph: Bilateral hilar lymphadenopathy. Reticular infiltrates.
- Biopsy: non-caseating granulomas
Treatment: Steroids |
Lesson Intro Video
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